in case of phenylalanine hydroxylase enzyme absence ------> accumulation of
phenylalanine without formation of tyrosin
2 pathways for dopa
tyrosin-----> dopa---->dopaquinon------>dopachrome------>melanine
tyrosin----->dopa--_co2--->dopamine---->noradrenaline---->adrenaline
pepck----->phosphoenolpyruvic carboxylase enz
.
a.a enter in tripeptide syth -----> glycine cystiene glutamic
a.a enter in coash synth.--------> b alanine cystien due to co2 of thioethanolamine
a.a enter detoxification------->glycine cystiene
a.a give formic acid------>glycin through glyoxalic acid
tryptophan by tryptophan dioxygenase
a.a share in formation of bile salts glycin cystien
phenylalanine without formation of tyrosin
2 pathways for dopa
tyrosin-----> dopa---->dopaquinon------>dopachrome------>melanine
tyrosin----->dopa--_co2--->dopamine---->noradrenaline---->adrenaline
pepck----->phosphoenolpyruvic carboxylase enz
.
a.a enter in tripeptide syth -----> glycine cystiene glutamic
a.a enter in coash synth.--------> b alanine cystien due to co2 of thioethanolamine
a.a enter detoxification------->glycine cystiene
a.a give formic acid------>glycin through glyoxalic acid
tryptophan by tryptophan dioxygenase
a.a share in formation of bile salts glycin cystien